Catera P, Tammaro V, Coletta S, Esposito G, Capasso S, Antonelli F
Dipartimento di Pediatria, Ospedale A. Cardarelli, Napoli, Italia.
Pediatr Med Chir. 1994 Jan-Feb;16(1):89-91.
Three infants suffering from hepatosplenomegaly, pancytopenia, hyperlipidemia, low fibrinogen levels and fever are reported. Two patients died during the first year of life, the third one received allogenic bone transplantation and survives. Clinical and haematological features are consistent with diagnosis of hemophagocytic lymphohistiocytosis.
报告了3例患有肝脾肿大、全血细胞减少、高脂血症、纤维蛋白原水平降低和发热的婴儿。2例患者在生命的第一年死亡，第3例接受了同种异体骨移植并存活。临床和血液学特征与噬血细胞性淋巴组织细胞增生症的诊断相符。
