Bilateral congenital grouped pigmentation of the retina in a patient with left superior rectus muscle palsy.

A 39-year-old man with left superior rectus muscle palsy had many sharply circumscribed, variable-sized pigmented spots in both fundi. His visual acuity, visual fields, and color vision appeared normal bilaterally. The electroretinographic responses were also normal. His family members were unaffected by pigmented spots in the retina. We believe that the bilateral congenital grouped pigmentation of the retina found in our patient may be rare.