Odero A, Chierichetti F, Canidio E, Savasta S
Divisione Chirurgia Vascolare, IRCCS Policlinico S. Matteo, Pavia, Italy.
Cardiovasc Surg. 1993 Jun;1(3):270-2.
A 2-year-old girl with asymmetrical upper limbs and underdevelopment of the bones of the left forearm, wrist and hand with associated muscular and osteal hypoplasia is described. Doppler ultrasonography of the arterial trunks of the upper limb suggested a normal ulnar trunk in the left upper arm, an arterial vessel extending from the bend of the elbow to the distal third of the forearm, and the absence of any other arterial trunks in the radial region. Angiography confirmed that vascularization of the forearm was sustained by the ulnar artery, which supported the dorsal arch of the carpus and digital arteries arising from it. The interosseal artery was morphologically normal but there was aplasia of the radial artery. It is suggested that this malformation is the result of suppressed development of the vascular system of the left radial segment as other pathologies normally associated with the condition were absent.
本文描述了一名2岁女童，其上肢不对称，左前臂、手腕和手部骨骼发育不全，并伴有肌肉和骨质发育不全。上肢动脉干的多普勒超声检查显示，左上臂尺动脉干正常，一条动脉血管从肘部弯曲处延伸至前臂远端三分之一处，桡侧区域未见其他动脉干。血管造影证实，前臂的血供由尺动脉维持，尺动脉为腕背弓和由此发出的指动脉提供支持。骨间动脉形态正常，但桡动脉发育不全。提示这种畸形是左桡侧段血管系统发育受抑制的结果，因为通常与该病症相关的其他病理情况并不存在。
