Adamsbaum C, Rolland Y, Josso N, Kalifa G
Radiology Department, Saint Vincent de Paul Hospital, Paris, France.
Pediatr Radiol. 1993;23(1):55-6. doi: 10.1007/BF02020225.
We report three cases of persistent Müllerian duct syndrome, which is a rare form of inherited male pseudohermaphroditism characterized by the presence of a uterus and tubes in otherwise normally virilized 46,XY males. We emphasize the usefulness of ultrasonographic study of the pelvis and inguinal areas in the preoperative diagnosis, which is difficult. We recommend that ultrasound be performed routinely in bilaterally cryptorchid patients.
我们报告了三例持续性苗勒管综合征病例,这是一种罕见的遗传性男性假两性畸形,其特征是在其他方面正常男性化的46,XY男性中存在子宫和输卵管。我们强调超声检查骨盆和腹股沟区域在术前诊断中的有用性,而术前诊断较为困难。我们建议对双侧隐睾患者常规进行超声检查。