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汗疱状大疱性类天疱疮

[Dyshidrosiform bullous pemphigoid].

作者信息

Mohr C, Duschet P, Bonsmann G, Luger T A, Gschnait F, Schwarz T

机构信息

Hautklinik, Westfälischen-Wilhelms-Universität, Münster.

出版信息

Hautarzt. 1993 Dec;44(12):785-8.

PMID:8113043
Abstract

Dyshydrosiform bullous pemphigoid is a clinical variant of bullous pemphigoid in which the lesions appear primarily on palms and soles. Knowledge of this unusual manifestation of bullous pemphigoid may be of practical relevance, since it has to be included in the differential diagnosis of blistering palmoplantar dermatoses. The correct diagnosis is confirmed by histological examination and immunofluorescence, which reveal all the characteristic hallmarks of bullous pemphigoid. Three patients with dyshydrosiform bullous pemphigoid are presented; clinical and histological aspects, findings on immunofluorescence, differential diagnosis and therapy are discussed.

摘要

汗疱状大疱性类天疱疮是大疱性类天疱疮的一种临床变体,其皮损主要出现在手掌和足底。了解大疱性类天疱疮的这种不寻常表现可能具有实际意义,因为它必须列入掌跖部水疱性皮肤病的鉴别诊断中。组织学检查和免疫荧光检查可确诊,这些检查揭示了大疱性类天疱疮的所有特征性标志。本文介绍了3例汗疱状大疱性类天疱疮患者;讨论了临床和组织学方面、免疫荧光检查结果、鉴别诊断及治疗。

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引用本文的文献

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Dyshidrosiform Bullous Pemphigoid.
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