Corbally M T, Heaton N, Rela M, Mieli-Vergani G, Portmann B, Mowat A, Williams R, Tan K C
Liver Transplant Surgical Service, King's College Hospital, London.
Arch Dis Child. 1994 Feb;70(2):147-8. doi: 10.1136/adc.70.2.147.
Three patients with stable liver function after Kasai portoenterostomy developed acute liver failure secondary to liver necrosis. Doppler ultrasound at presentation revealed reversed diastolic hepatic arterial blood flow. Two patients survived after urgent liver transplantation. Liver necrosis should be suspected in children with chronic liver disease presenting with fever and rapidly deteriorating liver function.
三名在肝门空肠吻合术后肝功能稳定的患者继发肝坏死而发展为急性肝衰竭。就诊时的多普勒超声显示肝动脉舒张期血流逆转。两名患者在紧急肝移植后存活。对于患有慢性肝病且出现发热和肝功能迅速恶化的儿童,应怀疑肝坏死。