Anagnostopoulos D, Valioulis I, Sfougaris D, Malliaropulos N, Foroglou P, Spyridakis G, Kallergis K
Clinique de Chirurgie Pédiatrique, Université de Thessalonique, Grèce.
Bull Assoc Anat (Nancy). 1993 Jun;77(237):5-7.
Of 152 patients with imperforate anus, 16 girls -25%), 10 boys (15%) have an abnormality of the genital tract and real frequency seems underevaluated. In girls, vaginal septum, bicornuate and didelphys uterus are mostly diagnosed, associated with severe unilateral upper urinary tract malformations. Absent vagina and uterus (Rokitansky syndrome) must be seen at birth, to preserve perineal fistula used to fashion a vagina at the time of the abdomino-perineal fistula pull through. In boys hypospadias, ectopia and uretero-vas anastomosis are the most frequent malformations.
在152例肛门闭锁患者中，16名女孩（25%）和10名男孩（15%）存在生殖道异常，实际发生率似乎被低估了。在女孩中，最常诊断出阴道纵隔、双角子宫和双子宫，并伴有严重的单侧上尿路畸形。无阴道和子宫（罗基坦斯基综合征）必须在出生时就被发现，以便在腹会阴瘘拖出术时保留会阴瘘，用于构建阴道。在男孩中，尿道下裂、异位和输尿管输精管吻合是最常见的畸形。
