Xu D Y, Zhan A L, Feng W H
Department of Radiology, Affiliated Hospital, Qingdao Medical College.
Chin Med J (Engl). 1993 Nov;106(11):871-5.
Four cases of systemic fibrous dysplasia were selected from 356 cases of fibrous dysplasia. All of them were verified pathologically. In these 4 cases, the long, short, flat and irregular bones were involved. Some of the changes were characteristic in comparison with those of the monostotics or regional types. This disorder was often seen clinically in females, started in early childhood and exacerbated during puberty. Its main symptoms were primary or secondary deformities. Radiologically, the main changes were diffuse and uniform expansion and developmental disturbances of the bones and joints.
从356例骨纤维异常增殖症病例中选取了4例系统性骨纤维异常增殖症病例。所有病例均经病理证实。在这4例病例中,长骨、短骨、扁骨和不规则骨均受累。与单骨型或区域型相比,其中一些变化具有特征性。这种疾病在临床上多见于女性,起病于儿童早期,在青春期加重。其主要症状为原发性或继发性畸形。放射学上,主要变化为骨骼和关节的弥漫性、均匀性膨胀以及发育障碍。