严重先天性神经肌肉疾病所致的早发性呼吸衰竭。
Early-onset respiratory failure caused by severe congenital neuromuscular disease.
作者信息
Sandler D L, Burchfield D J, McCarthy J A, Rojiani A M, Drummond W H
机构信息
Department of Pediatrics, Univeristy of Florida College of Medicine, Gainesville.
出版信息
J Pediatr. 1994 Apr;124(4):636-8. doi: 10.1016/s0022-3476(05)83148-8.
PMID:8151483
Abstract
Two unrelated infants with low Apgar scores, pneumothoraces, and severe pulmonary hypertension were treated with extracorporeal membrane oxygenation while receiving chemical sedation and neuromuscular paralysis. After decannulation from extracorporeal membrane oxygenation, hypotonia and hypoventilation persisted. Neurologic evaluation confirmed that both infants had a congenital myopathy.
摘要
两名无亲缘关系的婴儿，阿氏评分低、患有气胸和重度肺动脉高压，在接受化学镇静和神经肌肉麻痹治疗的同时接受了体外膜肺氧合治疗。在脱离体外膜肺氧合插管后，肌张力减退和通气不足持续存在。神经学评估证实这两名婴儿均患有先天性肌病。
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