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[特发性骨髓纤维化病程中伴有巨核细胞聚集的脾瘤]

[Splenoma with accumulation of megakaryocytes during the course of an idiopathic myelofibrosis].

作者信息

Brouland J, Molina T, Delmer A, Zittoun R, Diebold J

机构信息

Service Central Jacques-Delarue, d'Anatomie et de Cytologie Pathologiques, Hôtel-Dieu, Paris.

出版信息

Ann Pathol. 1994;14(1):32-5.

PMID:8155190
Abstract

We report a splenoma associated with an important megakaryocyte sequestration in peliotic sinuses. The diagnosis was done on surgical specimen of splenectomy performed for a painful splenomegaly occurring in a 71-year-old man presenting a primary idiopathic myelofibrosis. Histopathological features of these splenic microvascularization disorders, mainly occurring during hemopathy involving the spleen, are discussed. This case seems to confirm the hypothesis that splenoma could be an acquired splenic disease.

摘要

我们报告了一例与脾血池内重要的巨核细胞滞留相关的脾瘤。该诊断基于对一名71岁患有原发性特发性骨髓纤维化且因脾脏肿大疼痛而行脾切除术的手术标本。本文讨论了这些主要发生在累及脾脏的血液病期间的脾微血管化障碍的组织病理学特征。该病例似乎证实了脾瘤可能是一种后天性脾脏疾病的假说。

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