Goedde T A, Bumpers H, Fiscella J, Rao U, Karakousis C P
Department of Surgical Oncology, Roswell Park Cancer Institute, Buffalo, New York 14263.
J Surg Oncol. 1994 Apr;55(4):261-4. doi: 10.1002/jso.2930550413.
Eccrine porocarcinoma, a malignancy of the eccrine sweat glands, is extremely rare. Our report and a review of the literature (70 cases) emphasize the features of this tumor. Age at time of treatment ranged from 19 to 94 years (mean 67 years). Duration of the lesion ranged from two months to 50 years; 31 (44%) had the lesion present > or = 5 years. Forty-four patients (62%) had tumors located on the extremities, 13 (19%) on the head and neck region and 12 (17%) on the trunk. All patients whose race is known were white. Primary treatment should consist of wide local excision and regional lymphadenectomy, if clinically indicated. Although there is a significant risk of cutaneous, regional lymph node, or visceral metastases, the value of elective or therapeutic regional lymphadenectomy is unknown, as is the role of adjunctive therapy.
小汗腺汗孔癌是小汗腺的一种恶性肿瘤，极为罕见。我们的报告以及对文献（70例）的回顾强调了该肿瘤的特征。治疗时的年龄范围为19至94岁（平均67岁）。病变持续时间为两个月至50年；31例（44%）病变存在时间≥5年。44例患者（62%）的肿瘤位于四肢，13例（19%）位于头颈部区域，12例（17%）位于躯干。所有已知种族的患者均为白人。如果临床有指征，主要治疗应包括广泛局部切除和区域淋巴结清扫术。尽管存在皮肤、区域淋巴结或内脏转移的显著风险，但选择性或治疗性区域淋巴结清扫术的价值尚不清楚，辅助治疗的作用也不明确。
