Nakajima M
Department of Neurology, School of Medicine, Chiba University.
Rinsho Shinkeigaku. 1993 Dec;33(12):1313-6.
Ten patients with paraparesis due to peripheral neuropathies showed an unusual symptom characterized by an inability to stand still despite the ability to walk. The symptom was transient in the eight cases recovering from profound paraparesis due to acute or subacute polyneuropathies, and has continued for several years in two chronic polyneuropathy cases who have been suffering over ten years. All the patients take a series of to-and-fro steps forward and backward while standing until they initiate locomotion. We call this symptom "astasia without abasia", or the "stilts phenomenon", because the symptom reminds us of children's play with stilts. Weakness of the lower limbs was predominant in the ankle joints and muscle strength about the hip joints was relatively preserved. This pattern of weakness produced abnormal mechanical properties of the body in an upright posture. Postural movements of the patients thus consisted mainly of the movement about the hip joints (hip sway). The movement about the ankle joints (ankle sway) which maintains forward and backward leaning in upright posture was impaired. Although clinical examination revealed no significant sensory disturbances, impairment of the somatosensory system which stabilizes postural sway was proven in four patients by antero-posterior sway components around 1 Hz. Astasia without absia consists of maintaining body mass not on a fixed base but on a moving one. BOth abnormalities of postural movements and defective somatosensory feedback for postural stabilization may be responsible for this symptom.
10例因周围神经病变导致轻截瘫的患者表现出一种异常症状,其特征为尽管能够行走,但无法静止站立。在8例因急性或亚急性多发性神经病而从严重轻截瘫中恢复的患者中,该症状是短暂的,而在2例患有慢性多发性神经病且病程超过10年的患者中,该症状持续了数年。所有患者在站立时都会前后反复地来回踱步,直到开始行走。我们将这种症状称为“站立不能伴步行不能”,或“高跷现象”,因为这种症状让我们联想到孩子们玩高跷的情景。下肢无力在踝关节处最为明显,而髋关节周围的肌肉力量相对保留。这种无力模式在直立姿势下产生了身体异常的力学特性。因此,患者的姿势运动主要由髋关节周围的运动(髋部摆动)组成。维持直立姿势时前后倾斜的踝关节周围运动(踝关节摆动)受到损害。尽管临床检查未发现明显的感觉障碍,但通过1Hz左右的前后摆动分量,在4例患者中证实了稳定姿势摆动的体感系统存在损害。站立不能伴步行不能包括身体质量不是保持在固定的基础上,而是保持在移动的基础上。姿势运动异常和姿势稳定的体感反馈缺陷可能是导致这种症状的原因。