Santos A C, Bárbara C, Mendes B, Gomes M J, Amaral-Marques R
Departamento de Pneumologia, Hospital de Pulido Valente, Lisboa.
Acta Med Port. 1994 Feb;7(2):103-6.
The authors present a clinical case of Lymphangioleiomyomatosis of the lung. They analyse the clinical, radiological and functional features and comment on the evolution and therapeutic approach of this rare disorder. To the authors, lung involvement as well as therapeutic decision are important features that affect the prognosis.
作者介绍了一例肺淋巴管平滑肌瘤病的临床病例。他们分析了该罕见疾病的临床、放射学和功能特征,并对其病情发展和治疗方法进行了评论。在作者看来,肺部受累情况以及治疗决策是影响预后的重要因素。