Rojas R, Martin C, Roman J, Garcia J M, Marchal T, Torres A
Department of Haematology, Reina Sofia Hospital, Cordoba, Spain.
Br J Haematol. 1994 Feb;86(2):431-2. doi: 10.1111/j.1365-2141.1994.tb04762.x.
Castleman's disease (CD) is a rare disease of unknown aetiology and pathogenesis. We present an unusual case of abdominal CD in whom the first manifestation was an autoimmune haemolytic anaemia presenting 9 years before the diagnosis. The Coombs test became negative 2 months after surgical resection of the mass, suggesting that the mass was the source of the autoantibody. CD may be present in autoimmune haemolytic anaemia in patients with no evidence of any other disease.
卡斯特曼病(CD)是一种病因和发病机制不明的罕见疾病。我们报告了一例不寻常的腹部CD病例,其首发表现为自身免疫性溶血性贫血,在诊断前9年出现。肿块手术切除2个月后,库姆斯试验转为阴性,提示肿块是自身抗体的来源。在没有任何其他疾病证据的患者中,自身免疫性溶血性贫血可能伴有CD。