Koike H, Müller S C, Hohenfellner R
Department of Urology, Johannes Gutenberg University Medical School, Mainz, FRG.
Eur Urol. 1994;25(3):183-8. doi: 10.1159/000475280.
14 patients with renal angiomyolipoma are presented. Two of them had tuberous sclerosis (TS) with synchronous bilateral and multiple tumors. Two other patients without TS also had multiple tumors in 1 kidney. More than half the patients were symptomatic (n = 8), 2 of them with spontaneous rupture of the tumor. Misdiagnosis, spontaneous rupture and tumor growth can be prevented by utilizing conservative, organ-sparing techniques. In cases of solitary kidneys with large and/or hemorrhagic angiomyolipoma, superselective arterial embolization is indicated.
本文报告了14例肾血管平滑肌脂肪瘤患者。其中2例患有结节性硬化症（TS），伴有同步双侧多发肿瘤。另外2例无TS的患者也在一侧肾脏出现多发肿瘤。超过半数患者有症状（n = 8），其中2例肿瘤自发破裂。采用保守的保留器官技术可预防误诊、自发破裂和肿瘤生长。对于孤立肾合并大的和/或出血性血管平滑肌脂肪瘤的病例，建议进行超选择性动脉栓塞。
