丑角样鱼鳞病患儿的管理与随访
Management and follow-up of harlequin siblings.
作者信息
Prasad R S, Pejaver R K, Hassan A, al Dusari S, Wooldridge M A
机构信息
Department of Paediatrics, North West Armed Forces Hospital, Tabuk, Saudi Arabia.
出版信息
Br J Dermatol. 1994 May;130(5):650-3. doi: 10.1111/j.1365-2133.1994.tb13114.x.
Harlequin fetus is a rare clinical entity, and survival of affected infants beyond the first year of life is uncommon. Management involves intensive care of the skin and eyes, close monitoring of fluid and electrolyte status, constant support and counselling of parents, and surveillance against infection and side-effects of medication. A well-coordinated multidisciplinary approach can prolong survival beyond the neonatal period. We report our experiences in the management and follow-up of two successive harlequin siblings.
丑角样鱼鳞病是一种罕见的临床病症，受影响的婴儿存活超过一岁的情况并不常见。治疗包括对皮肤和眼睛的重症护理、密切监测液体和电解质状况、持续为父母提供支持和咨询，以及预防感染和药物副作用。精心协调的多学科方法可延长新生儿期后的生存期。我们报告了对连续两名患丑角样鱼鳞病的兄弟姐妹进行治疗和随访的经验。
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