Kanev P M, Getch C C, Jallo J, Faerber E N
Department of Neurosurgery, Temple University School of Medicine, Philadelphia, Pa.
Pediatr Neurosurg. 1994;20(3):214-6. doi: 10.1159/000120791.
A 13-year-old female presented with acute left gaze paralysis. MRI revealed hydrosyringomyelia (HSM) with syringobulbia in the left pons extending cephalad into the centrum semiovale. A suboccipital craniotomy was performed and the foramen of Magendie was imperforate. Ocular movements normalized in 2 months and postoperative MRI confirmed resolution of the cerebral syrinx and syringobulbia and diminished HSM. This case represents an extreme example of the altered spinal fluid dynamics with Chiari I malformation. Theories on HSM are reviewed.
一名13岁女性出现急性左侧凝视麻痹。磁共振成像（MRI）显示患有脊髓空洞症（HSM），伴有左侧脑桥的延髓空洞症，向上延伸至半卵圆中心。进行了枕下开颅手术，发现马根迪孔闭锁。2个月内眼球运动恢复正常，术后MRI证实脑脊髓空洞和延髓空洞消失，脊髓空洞症减轻。该病例代表了Chiari I型畸形脑脊液动力学改变的一个极端例子。本文对脊髓空洞症的相关理论进行了综述。
