Toren A, Kende G, Mandel M, Biniaminov M, Brok-Simoni F, Rosenthal E, Engelberg I, Neumann Y, Kenet G, Ben-Bassat I
Institute of Hematology, Chaim Sheba Medical Center, Tel-Hashomer, Israel.
Leukemia. 1994 Jun;8(6):1062-4.
Two cases are described that provide further evidence for clonal evolution in pre-B-cell acute lymphoblastic leukemia. Two infants, whose lymphoblasts at diagnosis were morphologically subtyped as L1 and immunophenotyped as HLA DR+, CD19+, CD10+/- and C mu-, were induced and maintained in remission. One child relapsed 6 months after initiation of therapy. This time his lymphoblasts had L3 morphology and immunophenotyping demonstrated the appearance of surface immunoglobulins. The second child relapsed 18 months after initiation of therapy with a lymphomatous picture. He also had peripheral and bone marrow blasts with L3 morphology and surface immunoglobulins. A lymph node biopsy showed diffuse small non-cleaved lymphoma with a 'starry sky' appearance compatible with Burkitt's lymphoma. Only one case with a similar clonal evolution has been reported in the literature, but no surface immunoglobulins were demonstrated. The significance of clonal evolution in these cases and its potential practical implications are discussed.
本文描述了两例病例,为前B细胞急性淋巴细胞白血病的克隆进化提供了进一步证据。两名婴儿,诊断时其原始淋巴细胞形态学亚型为L1,免疫表型为HLA DR+、CD19+、CD10+/-和Cμ-,诱导缓解并维持缓解状态。一名儿童在治疗开始6个月后复发。此时他的原始淋巴细胞具有L3形态,免疫表型显示出现表面免疫球蛋白。第二名儿童在治疗开始18个月后以淋巴瘤表现复发。他的外周血和骨髓原始淋巴细胞也具有L3形态和表面免疫球蛋白。淋巴结活检显示弥漫性小无裂细胞淋巴瘤,呈“星空”样外观,符合伯基特淋巴瘤。文献中仅报道过一例类似的克隆进化病例,但未证实有表面免疫球蛋白。本文讨论了这些病例中克隆进化的意义及其潜在的实际影响。