Hamdi A, Nouri A, Selmi M, Zouari K, Belghith M, Nouri K, Bchir S, Tabka M A
Ann Chir. 1993;47(6):553-6.
Cystic lymphangioma is a rare tumour (6% of benign tumours in children), frequently situated in the cervical or axillary region and exceptionally intraabdominal. It arises due to a congenital defect in the connection of the primary lymphatic channels with the central collecting system. It presents clinically either in the form of a pseudo-appendix or pseudo-ascites syndrome or in the form of an abdominal tumour with or without compression of adjacent structures. It can now be easily diagnosed by ultrasonography. Treatment is well defined and consists of surgical resection of the isolated lymphangioma or associated with the adjacent intestine, depending on the site of the tumour. It has a good prognosis.
囊性淋巴管瘤是一种罕见的肿瘤（占儿童良性肿瘤的6%），常位于颈部或腋窝区域，极少位于腹腔内。它是由于初级淋巴管与中央收集系统连接的先天性缺陷而产生的。临床上它表现为假性阑尾或假性腹水综合征的形式，或者表现为腹部肿瘤，伴有或不伴有对相邻结构的压迫。现在通过超声检查很容易诊断。治疗方法明确，根据肿瘤的部位，包括对孤立的淋巴管瘤或与相邻肠道相连的淋巴管瘤进行手术切除。其预后良好。
