苍白球和黑质双侧受累的Hallervorden-Spatz病：磁共振成像表现

Hallervorden-Spatz disease with bilateral involvement of globus pallidus and substantia nigra: MR demonstration.

作者信息

Porter-Grenn L, Silbergleit R, Mehta B A

机构信息

Department of Diagnostic Radiology, Henry Ford Hospital, Detroit, MI 48202.

出版信息

J Comput Assist Tomogr. 1993 Nov-Dec;17(6):961-3. doi: 10.1097/00004728-199311000-00019.

DOI:10.1097/00004728-199311000-00019

PMID:8227584

Abstract

Hallervorden-Spatz disease presents with relentless mental and physical deterioration. Pathologically there is abnormal iron deposition in the globi pallidi, substantia nigra, and red nuclei. A spectrum of abnormal basal ganglia signal intensities have been described on MRI. A pediatric case with low signal intensity in the globi pallidi and substantia nigra is presented.

摘要

哈勒沃登-施帕茨病表现为持续的精神和身体衰退。病理上，苍白球、黑质和红核存在异常铁沉积。MRI上已描述了一系列基底节异常信号强度。本文介绍了一例苍白球和黑质呈低信号强度的儿科病例。