囊性纤维化是一种酸性黏多糖贮积症吗？
Is cystic fibrosis an acid mucopolysaccharidosis?
作者信息
Mukherji R N, Moss P H, Heffernan C K
出版信息
Arch Dis Child. 1976 Jul;51(7):563-5. doi: 10.1136/adc.51.7.563.
Abstract
A case of cystic fibrosis with myocardial fibrosis and acid mucopolysaccharide deposits in the myocardium is described. The case supports the theory that cystic fibrosis may be a genetic acid mucopolysaccharidosis.
摘要
本文描述了一例患有心肌纤维化和心肌酸性粘多糖沉积的囊性纤维化病例。该病例支持囊性纤维化可能是一种遗传性酸性粘多糖贮积症的理论。
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Is cystic fibrosis an acid mucopolysaccharidosis?囊性纤维化是一种酸性黏多糖贮积症吗？
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本文引用的文献
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Cystic fibrosis of the pancreas complicated by myocardial fibrosis.胰腺囊性纤维化并发心肌纤维化。
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Myocardial fibrosis in cystic fibrosis of the pancreas.胰腺囊性纤维化中的心肌纤维化。
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