放射学病例研究。巨脂性营养障碍。

Radiologic case study. Macrodystrophia lipomatosa.

作者信息

Hildebrandt J W, Olson P, Paratainen H, Griffiths H J

机构信息

Department of Radiology, University of Minnesota, Minneapolis 55455.

出版信息

Orthopedics. 1993 Sep;16(9):1075-7. doi: 10.3928/0147-7447-19930901-18.

DOI:10.3928/0147-7447-19930901-18

PMID:8234076

Abstract

Macrodystrophia lipomatosa is a rare form of gigantism involving an extremity consisting of predominately fibroadipose tissue. Radiographically, it appears as hypertrophy of soft tissues and bone. CT and MR scanning delineate the tissues involved and are virtually diagnostic, demonstrating the predominantly adipose component as well as the overgrowth of the bones, nerves, and vessels also involved.

摘要

巨脂性营养障碍是一种罕见的巨人症形式，累及一个主要由纤维脂肪组织构成的肢体。在影像学上，它表现为软组织和骨骼肥大。CT和磁共振扫描可描绘出受累组织，几乎具有诊断性，显示出主要的脂肪成分以及同时受累的骨骼、神经和血管的过度生长。