Weitzner S
Am Surg. 1976 Nov;42(11):866-70.
A 24-year-old man with neurofibromatosis and adjacent malignant schwannoma and neurofibroma of an intrathoracic vagus is reported. He survived for eight months, developing massive recurrence three months after surgical extirpation. Review of the 13 previously documented patients with neurofibroma of the intrathoracic vagus indicates that most patients have neurofibromatosis. The thickest portion of the intrathoracic vagi, the proximal portions and most often the left nerve, is the site of predilection. In about half, multiple neurofibromata of the nerve may be present. Malignant schwannoma of the mediastinum is discussed and it would appear that neurofibromatosis is not a predisposing factor.
报道了一名24岁患有神经纤维瘤病的男性，其胸腔内迷走神经伴有相邻的恶性神经鞘瘤和神经纤维瘤。他存活了8个月，在手术切除3个月后出现大量复发。对之前记录的13例胸腔内迷走神经神经纤维瘤患者的回顾表明，大多数患者患有神经纤维瘤病。胸腔内迷走神经最粗的部分、近端部分以及最常见的左侧神经是好发部位。约半数患者神经可能存在多个神经纤维瘤。文中讨论了纵隔恶性神经鞘瘤，似乎神经纤维瘤病不是一个易感因素。
