Dupuis C, Charaf L A, Abou C P, Brevière G M
Service de cardiologie infantile, Hôpital cardiologique, Lille.
Arch Mal Coeur Vaiss. 1993 May;86(5):541-7.
The authors report the results of a cooperative study of 37 operated cases of the scimitar syndrome. The diagnostic procedures, the operative indications, the surgical indications, the postoperative complications and the long-term outcome were reviewed. The results were disappointing irrespective of the surgical technique that was used (reimplantation of the right pulmonary veins in the left atrium, lobectomy, pneumonectomy). Only 12 patients had a satisfactory postoperative outcome and good long-term results; 21 patients had long-term chronic respiratory failure with a reduced exercise capacity and 4 patients died after surgery. Of the 21 patients with long-term sequellae, 17 had a thrombosis of the anastomosis between the right pulmonary veins and the left atrium; this occurred immediately after surgery.
作者报告了一项关于37例弯刀综合征手术病例的合作研究结果。回顾了诊断程序、手术指征、外科手术指征、术后并发症及长期预后。无论采用何种手术技术（右肺静脉再植入左心房、肺叶切除术、全肺切除术），结果均令人失望。只有12例患者术后结果满意且长期效果良好；21例患者出现长期慢性呼吸衰竭，运动能力下降，4例患者术后死亡。在21例有长期后遗症的患者中，17例右肺静脉与左心房之间的吻合处发生血栓形成，这在术后立即出现。
