Skovby F, Graham J M, Sonne-Holm S, Cohen M M
Department of Pediatrics, Rigshospitalet, Copenhagen, Denmark.
Am J Med Genet. 1993 Oct 1;47(5):656-9. doi: 10.1002/ajmg.1320470516.
We report on 2 children with spinal stenosis and neurologic sequelae. They illustrate the 2 ways in which spinal compromise may develop in Proteus syndrome--vertebral anomalies or tumor infiltration. In one patient, spinal stenosis resulted from an angular kyphoscoliosis. In the other, cord compression resulted from infiltration of a paraspinal, intrathoracic angiolipoma.
我们报告了2例患有脊柱狭窄和神经后遗症的儿童。他们说明了变形综合征中脊柱受损可能发展的两种方式——椎体异常或肿瘤浸润。在1例患者中，脊柱狭窄是由角状脊柱后凸侧弯引起的。在另1例患者中，脊髓受压是由胸段脊柱旁血管脂肪瘤浸润所致。
