Seewann H L
Medizinischen Abteilung des a. ö. Landeskrankenhauses Fürstenfeld.
Wien Med Wochenschr. 1993;143(16-17):420-4.
Interferon-alpha (IFN-alpha) exhibits a clear platelet reductive effect in patients with essential thrombocythemia as well as in other chronic myeloproliferative disorders with thrombocytosis. In a total of 51 patients with chronic myeloproliferative disorders with thrombocytosis we analyzed the effect of IFN-alpha in respect to platelet reduction, remission rates, induction- and maintenance dosage, long term tolerance and side effects. According to our classification CML 6, chronic mega-karyocytic granulocytic myelosis 5, essential thrombocythemia 26 and polycythemia vera 15 patients were treated. Treatment consisted of induction with 3 or 5 MU IFN-alpha daily followed by a maintenance therapy with 3 or 5 MU thrice weekly. Platelet reduction was found in all patients, CR (platelets < 450 G/l) in 78%. Within 2 months of induction therapy, CR in patients treated with 5 MU IFN daily was found in 75% compared to 52% in patients treated with 3 MU IFN daily. Dosage reduction in maintenance periode caused an increase of platelets to more than 450 G/l in 39% of patients. Out of 40 Philadelphia-negative chronic myeloproliferative disorders treated for more than 3 months in 10 patients treatment was disrupted after 5 to 18 months because of the following side effects: nausea, fatigue, vertigo, fever, headache, diarrhea, anorexia, heartburn, hairloss, myalgia, and thrombocytopenia. Due to the mutagenic effect of alkylating cytostatics and Radiophosphorus, IFN-alpha treatment represents a first line strategy for chronic myeloproliferative disorders with thrombocytosis especially in younger patients who are symptomatic and in those who suffered from episodes of bleeding or thrombosis.
α干扰素(IFN-α)对原发性血小板增多症患者以及其他伴有血小板增多的慢性骨髓增殖性疾病具有明显的血小板减少作用。我们共分析了51例伴有血小板增多的慢性骨髓增殖性疾病患者,观察IFN-α在血小板减少、缓解率、诱导及维持剂量、长期耐受性和副作用方面的效果。根据我们的分类,治疗的患者中慢性粒细胞白血病(CML)6例、慢性巨核细胞粒细胞性骨髓增生症5例、原发性血小板增多症26例、真性红细胞增多症15例。治疗方法为每日用3或5百万单位(MU)IFN-α诱导,随后每周三次用3或5 MU维持治疗。所有患者均出现血小板减少,78%达到完全缓解(血小板<450 G/l)。诱导治疗2个月内,每日用5 MU IFN治疗的患者完全缓解率为75%,而每日用3 MU IFN治疗的患者为52%。维持期剂量减少后,39%的患者血小板增加至450 G/l以上。在40例接受治疗超过3个月的费城染色体阴性慢性骨髓增殖性疾病患者中,10例患者在5至18个月后因以下副作用中断治疗:恶心、疲劳、眩晕、发热、头痛、腹泻、厌食、烧心、脱发、肌痛和血小板减少。由于烷化剂和放射性磷的诱变作用,IFN-α治疗是伴有血小板增多的慢性骨髓增殖性疾病的一线治疗策略,尤其适用于有症状的年轻患者以及有出血或血栓形成发作的患者。