Boutsen Y, Richir C, Bernis P
Service de Médecine Interne, Hôpitaux St-Joseph, Gilly.
Acta Clin Belg. 1993;48(5):331-7. doi: 10.1080/17843286.1993.11718326.
Ureteral amyloidosis is an uncommon disease. It usually presents as an ureteral stenosis and resembles ureteral malignancy. The lesion consists of localized amyloidosis, containing lambda light chains, the etiology of which remains unknown. Ureteral calcifications have been suggested to be pathognomonic. When the diagnosis of ureteral amyloidosis is considered preoperatively, a renal-sparing surgery must be planned. We observed a case of bilateral ureteral amyloidosis presenting with anuria; the patient was treated with conservative surgery and colchicine. The renal function improved without recurrence and remained stable after 5 years of follow-up.
输尿管淀粉样变性是一种罕见疾病。它通常表现为输尿管狭窄,类似输尿管恶性肿瘤。病变由局部淀粉样变性组成,含有λ轻链,其病因尚不清楚。输尿管钙化被认为具有诊断意义。当术前考虑输尿管淀粉样变性的诊断时,必须规划保留肾脏的手术。我们观察到一例双侧输尿管淀粉样变性伴无尿的病例;该患者接受了保守手术和秋水仙碱治疗。肾功能改善且无复发,随访5年后保持稳定。