Zhou A
Shanghai Institute for Pediatric Research.
Zhonghua Yi Xue Za Zhi. 1993 Jul;73(7):393-5, 446.
Cardiac catheterization and angiography were performed in 31 patients with PA/IVS to evaluate the morphology of RV and hemodynamics. The age of patients ranged from 1 day to 39 month (mean 4.7 month). The patients were divided into three groups: mild (19.4%), moderate (64.5%) and severe (16.1%) RV hypoplasia, according to the degree of tricuspid valve and right ventricular hypoplasia. Seven of the 31 patients (22.6%) had right ventricular myocardial sinusoid-coronary artery fistula. The right and left ventricular pressures in 26 patients were measured simultaneously. The right ventricular pressures were supra-systemic in 18 patients (69.2%), systemic in 6 (23.1%), less than systemic pressures in 2 (7.7%); the others were PA/IVS with ASD(6 patients), PFO (25), PDA (25). Palliative and definitive operations were performed on 22 patients. The results show that determining the morphology of RV and the hemodynamics before operation is helpful in selecting appropriate operation for lowering the operative mortality.
对31例肺动脉闭锁合并室间隔完整（PA/IVS）患者进行了心导管检查和血管造影，以评估右心室形态和血流动力学。患者年龄从1天至39个月不等（平均4.7个月）。根据三尖瓣和右心室发育不全的程度，将患者分为三组：轻度右心室发育不全（19.4%）、中度（64.5%）和重度（16.1%）。31例患者中有7例（22.6%）存在右心室心肌窦状隙-冠状动脉瘘。同时测量了26例患者的右心室和左心室压力。18例患者（69.2%）右心室压力高于体循环压力，6例（23.1%）为体循环压力，2例（7.7%）低于体循环压力；其他患者为合并房间隔缺损（ASD，6例）、卵圆孔未闭（PFO，25例）、动脉导管未闭（PDA，25例）的PA/IVS。对22例患者实施了姑息性和根治性手术。结果表明，术前确定右心室形态和血流动力学有助于选择合适的手术方式以降低手术死亡率。
