Barbosa Filho J, Barbosa P R
Instituto Brasileiro de Cardiologia, Rio de Janeiro.
Arq Bras Cardiol. 1993 Aug;61(2):107-9.
A 48-years-old woman with Lutembacher syndrome with a clinical and laboratory finding of atrial septal defect, of the "ostium secundum" type and without pulmonary hypertension was reported. We observed, from diagnostic viewpoint, that the electrocardiographic finding of left atrial overload and the echocardiographic pattern of mitral stenosis where the most important diagnostic sign the mitral valve involvement. The patient underwent surgery and the atrial septal defect was closed with a patch. After the surgery the signs of atrial septal defect where very poor and the signs of mitral stenosis dominated the clinical picture of the patient. Although we did not make any intervention at the mitral valve, the patient had a good outcome and until the present date she is in functional class I.
报道了一名48岁患有鲁登巴赫综合征的女性,其临床和实验室检查发现为继发孔型房间隔缺损且无肺动脉高压。从诊断角度来看,我们观察到左心房负荷过重的心电图表现以及二尖瓣狭窄的超声心动图模式是二尖瓣受累的最重要诊断体征。该患者接受了手术,房间隔缺损用补片封闭。术后房间隔缺损的体征非常不明显,二尖瓣狭窄的体征在患者的临床表现中占主导。尽管我们未对二尖瓣进行任何干预,但患者预后良好,至今仍处于心功能I级。