Matsuyama Y, Saigusa N, Hioki M, Matsushima S, Tanaka S, Shoji T
Department of Thoracic and Cardiovascular Surgery, Hoya Kosei Hospital, Tokyo, Japan.
Nihon Kyobu Geka Gakkai Zasshi. 1994 Jan;42(1):144-9.
Scimitar syndrome is relatively uncommon syndrome. A 14-year-old female referred to our hospital for abnormal shadow of chest fluoroscopic examination. She had no symptom except cough due to bronchial asthma. Chest X-ray film showed Scimitar sign. Cardiac catheterization revealed 30% left to right shunt without atrial septal defect. Pulmonary angiography showed anomalous pulmonary vein was drained to inferior vena cava and left atrium. Surgical correction was attempted monitoring the pulmonary arterial pressure. Anomalous pulmonary vein and systemic arteries were ligated and divided at the level of diaphragm. Postoperative course was smooth. We have found 4 similar operated cases previously reported in the world.
弯刀综合征是一种相对罕见的综合征。一名14岁女性因胸部荧光透视检查发现异常阴影转诊至我院。除支气管哮喘引起的咳嗽外,她没有其他症状。胸部X线片显示弯刀征。心导管检查显示有30%的左向右分流,无房间隔缺损。肺血管造影显示异常肺静脉引流至下腔静脉和左心房。在监测肺动脉压的情况下尝试进行手术矫正。在膈肌水平结扎并切断异常肺静脉和体动脉。术后过程顺利。我们发现此前世界上曾报道过4例类似的手术病例。