Shian W J, Wang Y J, Chi C S
Department of Pediatrics, Taichung Veterans General Hospital, Taiwan, Republic of China.
Acta Paediatr. 1993 Apr;82(4):383-6. doi: 10.1111/j.1651-2227.1993.tb12702.x.
Hospital records of 24 Chinese infants and children (7 males and 17 females) with choledochal cysts were reviewed. The patients were aged 1 day to 17 years. Abdominal pain, palpable abdominal mass and jaundice, either alone or in combination, accounted for most of the initial presentations. Twenty-two patients were classified as type I with surgery, while the other two patients were type V without surgery. Ultrasonography is a rapid and accurate diagnostic method in the initial evaluation. Cyst excision with Roux-en-Y hepaticojejunostomy was the treatment of choice in this series. Chronic cholecystitis with or without inflammation of choledochal cyst was the most common pathological finding. Five patients underwent liver biopsies, showing four biliary cirrhosis and one portal fibrosis. So far, there is no evidence of malignancy in any patient.
回顾了24例中国婴幼儿(7例男性,17例女性)胆总管囊肿的医院记录。患者年龄为1天至17岁。腹痛、可触及的腹部肿块和黄疸,单独出现或合并出现,是大多数初始表现。22例患者经手术分类为I型,另外2例患者为V型,未接受手术。超声检查是初始评估中快速准确的诊断方法。囊肿切除加Roux-en-Y肝空肠吻合术是本系列的首选治疗方法。伴有或不伴有胆总管囊肿炎症的慢性胆囊炎是最常见的病理发现。5例患者接受了肝活检,显示4例胆汁性肝硬化和1例门脉纤维化。到目前为止,没有任何患者有恶性肿瘤的证据。