Steiner Z, Mares A J
Department of Pediatric Surgery, Soroka Medical Center, Beersheva, Israel.
Eur J Pediatr Surg. 1993 Apr;3(2):112-4. doi: 10.1055/s-2008-1063524.
Three unusual cases of large anterolateral congenital diaphragmatic hernia are described with emphasis on its embryogenesis. This type of diaphragmatic defect is rare and underemphasized. Its clinical spectrum ranges from the asymptomatic case to those with acute respiratory distress. It may present itself as a solitary defect or as part of a more complex association such as the thoracoabdominal syndrome. This defect should be differentiated from Morgagni (and other anterior) diaphragmatic hernias by its size and lateral extension and the presence of left pulmonary hypoplasia. Treatment is by primary operative repair, and prognosis depends on the presence and severity of associated malformations.
本文描述了三例罕见的先天性前外侧膈疝病例,并着重探讨了其胚胎发生机制。这种类型的膈肌缺损较为罕见且未得到足够重视。其临床症状范围从无症状到急性呼吸窘迫不等。它可能表现为孤立性缺损,或作为更复杂综合征(如胸腹综合征)的一部分。这种缺损应通过其大小、侧向延伸以及左肺发育不全的存在与莫尔加尼(及其他前部)膈疝相鉴别。治疗方法为一期手术修复,预后取决于相关畸形的存在及严重程度。