Saint-Paul M C, Gugenheim J, Hofman P, Arpurt J P, Fabiani P, Michiels J F, Fujita N, Goubeaux B, Loubière R, Delmont J
Service d'Anatomie Pathologique, Hôpital Pasteur, Nice.
Gastroenterol Clin Biol. 1993;17(3):218-22.
A 68 year old woman with primary hepatic leiomyosarcoma, impairement of general status and right upper quadrant pain was diagnosed with liver tumor by sonography, CT scan and nuclear magnetic resonance imaging. Angiograms showed a hypervascular tumor. The patient was treated by hepatic transplantation but died 15 days after operation. The diagnosis of leiomyosarcoma was established by immunohistochemical and ultrastructural studies; the primary nature was confirmed by necropsy. Diagnostic and therapeutic features of primary hepatic leiomyosarcoma--the 19th case reported in the literature--are discussed.
一名68岁患有原发性肝平滑肌肉瘤、一般状况不佳且右上腹疼痛的女性,通过超声检查、CT扫描和核磁共振成像被诊断出患有肝脏肿瘤。血管造影显示为高血管性肿瘤。该患者接受了肝移植治疗,但术后15天死亡。通过免疫组织化学和超微结构研究确诊为平滑肌肉瘤;尸检证实了其原发性。本文讨论了原发性肝平滑肌肉瘤的诊断和治疗特点——这是文献报道的第19例病例。