Adami P, Manzoni P, Rohmer P
Département de Radiologie Viscérale, Centre Hospitalier, Besançon.
Ann Radiol (Paris). 1993;36(2):129-33.
Ehlers-Danlos syndrome is one of the most frequent hereditary connective tissue diseases. Type 4 or Sack-Barabas syndrome differs by the seventy of arterial complications. The authors report a case of severely progressive aneurysms since thrombosis of the aneurysm of the left hepatic artery, splenic artery, and small aneurysms of the lower pancreatic artery and rapid development of severe ectasia of the coeliac trunk and the commun hepatic artery all occurred over a period of three months.
埃勒斯-当洛综合征是最常见的遗传性结缔组织疾病之一。4型或萨克-巴拉巴斯综合征的不同之处在于动脉并发症的严重程度。作者报告了一例病例，自左肝动脉、脾动脉的动脉瘤血栓形成以来，出现严重进展性动脉瘤，同时下胰动脉有小动脉瘤，并且在三个月的时间里，腹腔干和肝总动脉迅速出现严重扩张。
