Kikuchi S, Ajiki H, Morikawa M, Ohkawa Y, Sakai H, Kawamura H, Kawashima T, Baba M, Komatsu S, Sawada T
Department of Surgery (Section 2), Sapporo Medical College & Hospital, Japan.
Kyobu Geka. 1993 Jul;46(7):549-53; discussion 553-6.
Three patients with double-outlet right ventricle (DORV) and left ventricular outflow tract obstruction (LVOTO) were described. In each patient, LVOTO was produced by restrictive VSD which resulted from malalignment of the conal musculature and a discrete subaortic membrane. All patients underwent surgical repair with enlargement of the ventricular septal defect and rerouting of the outflow tract from the left ventricle to the aorta. One patient died of congestive heart failure three months postoperatively. Causes of LVOTO and surgical management of DORV with LVOTO were discussed.
本文描述了3例右心室双出口(DORV)合并左心室流出道梗阻(LVOTO)的患者。在每例患者中,LVOTO是由圆锥肌排列不齐和一个离散的主动脉下膜导致的限制性室间隔缺损(VSD)引起的。所有患者均接受了手术修复,包括扩大室间隔缺损以及将左心室流出道改道至主动脉。1例患者术后3个月死于充血性心力衰竭。文中讨论了LVOTO的病因以及DORV合并LVOTO的手术治疗方法。