Környei V, Kiss A, Kamarás J
Kaposi Mór Megyei Kórház Kaposvár Gyermekosztály, Országos Kardiológiai Intézet Gyermekosztály, Budapest.
Orv Hetil. 1993 Aug 1;134(31):1703-7.
Congenital absence of the pericardium, whether partial or total, is a rare abnormality. If suspicion of such a malformation arises it should be classified because of possible herniation of the atrium or ventricle. The authors report the case of an asymptomatic young male patient in whom the diagnosis was suggested radiographically, electrocardiographically (total electrical alternans has been noticed) and confirmed by cross-sectional echocardiography, computed tomography and magnetic resonance imaging. Only in exceptional cases should it be necessary to perform an exploratory thoracotomy. In patients with complete pericardial defects no specific therapy is indicated, however, in patients with partial defects surgical treatment is indicated. Congenital pericardial defects are not completely benign, as has been suggested before.
先天性心包缺失，无论是部分缺失还是完全缺失，都是一种罕见的异常情况。如果怀疑存在这种畸形，由于心房或心室可能发生疝出，应进行分类。作者报告了一例无症状的年轻男性患者，其诊断通过放射学、心电图（发现完全性电交替）以及经胸超声心动图、计算机断层扫描和磁共振成像得以证实。仅在特殊情况下才需要进行开胸探查术。对于完全性心包缺损的患者，无需进行特殊治疗，然而，对于部分缺损的患者，则需要进行手术治疗。先天性心包缺损并非如之前所认为的那样完全无害。
