Van Cutsem E
Department of Internal Medicine, University Hospital Gasthuisberg, Leuven.
Acta Gastroenterol Belg. 1993 Jan-Feb;56(1):2-10.
Gastrointestinal vascular malformations can cause haemorrhage requiring multiple transfusions. Surgical or endoscopic therapy are ineffective when the vascular malformations are spread diffusely over the gastrointestinal tract, when lesions escape identification or are not accessible for treatment. Several reports suggest that oestrogen-progesterone therapy is effective in the treatment of epistaxis in hereditary haemorrhagic telangiectasia. The aim of our studies is to test the hypothesis that oestrogen-progesterone is an effective treatment for bleeding gastrointestinal vascular malformations in patients with a very high transfusion need and in whom surgical or endoscopic treatment failed or could not be performed. The mean transfusion requirement prior to entering the studies amounted to 35.4 units packed per patient. In an uncontrolled trial oestrogen-progesterone therapy diminished significantly transfusion requirements from 3.4 units packed cells per patient per month to 0.1 units packed cells (p = 0.02). Haemorrhage ceased totally in 3 of 7 patients. A double-blind randomized placebo-controlled, cross-over trial shows that therapy with 0.050 mg ethinyloestradiol and 1 mg norethisterone is very effective in reducing transfusion requirements: 2.8 versus 11.2 units packed cells over a 6 month treatment period (p = 0.002). Only 3 of 13 patients treated with ethinyloestradiol and norethisterone required transfusions for persistent bleeding, while 12 of 13 patients in the placebo group had transfusion requirements (p = 0.001). After stopping hormonal therapy, no transfusions were needed for a mean of 10 months. This indicates a long-lasting effect of ethinyloestradiol and norethisterone on bleeding and transfusion requirements.(ABSTRACT TRUNCATED AT 250 WORDS)
胃肠道血管畸形可导致出血,需要多次输血。当血管畸形在胃肠道广泛分布、病变难以识别或无法进行治疗时,手术或内镜治疗无效。几项报告表明,雌激素 - 孕激素疗法对遗传性出血性毛细血管扩张症的鼻出血治疗有效。我们研究的目的是检验这一假设:对于输血需求极高且手术或内镜治疗失败或无法进行的胃肠道血管畸形出血患者,雌激素 - 孕激素是一种有效的治疗方法。进入研究前,每位患者的平均输血需求量达35.4单位浓缩红细胞。在一项非对照试验中,雌激素 - 孕激素疗法使输血需求量从每位患者每月3.4单位浓缩红细胞显著降至0.1单位浓缩红细胞(p = 0.02)。7名患者中有3名出血完全停止。一项双盲随机安慰剂对照交叉试验表明,0.050毫克炔雌醇和1毫克炔诺酮治疗在减少输血需求方面非常有效:在6个月的治疗期内,分别为2.8单位与11.2单位浓缩红细胞(p = 0.002)。接受炔雌醇和炔诺酮治疗的13名患者中,只有3名因持续出血需要输血,而安慰剂组13名患者中有12名有输血需求(p = 0.001)。停止激素治疗后,平均10个月无需输血。这表明炔雌醇和炔诺酮对出血和输血需求有持久影响。(摘要截选至250字)