Hucín B, Tláskal T, Horváth P, Kucera V, Kopecká L, Cvachovec K
Pediatrické kardiocentrum, FN v Motole, Praha.
Rozhl Chir. 1993 Apr;72(4):147-51.
Anatomical correction with an intraventricular tunnel, as suggested by Kawashima, was performed in 14 children with a double-outlet right ventricle and a subpulmonary (4) or non-committed (10) defect of the ventricular septum with one early and one late death. Nine children had previous palliative operations. Complications after radical surgery were residual ventricular defects (4), infectious endocarditis (2) and impaired rhythm (one sudden death). Twelve patients are after medium- term or long-term follow-up free from subjective complaints, ten children report good performance, in two the performance is slightly reduced. Anatomical intraventricular correction of double-outlet right ventricle restores the mitral valve and left ventricle to the systemic circulation. The prognosis of children with double-outlet right ventricle and subpulmonary or remote ventricular defect improves substantially.
按照川岛的建议,对14例右心室双出口合并室间隔肺下型(4例)或无顶型(10例)缺损的患儿进行了心室内隧道解剖矫正术,其中1例早期死亡,1例晚期死亡。9例患儿曾接受过姑息性手术。根治性手术后的并发症包括残余室间隔缺损(4例)、感染性心内膜炎(2例)和心律失常(1例猝死)。12例患者经过中期或长期随访后无主观不适,10例患儿表现良好,2例患儿表现略有下降。右心室双出口的心室内解剖矫正可使二尖瓣和左心室恢复至体循环。右心室双出口合并肺下型或远离型室间隔缺损患儿的预后有显著改善。