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先天性锁骨下动脉盗血综合征合并主动脉弓异常

Congenital subclavian steal syndrome with anomaly of the aortic arch.

作者信息

Yamakawa H, Nishikawa M, Nakahara I, Inagawa S, Koide T, Handa H

机构信息

Department of Neurosurgery, Hamamatsu Rosai Hospital, Shizuoka, Japan.

出版信息

Surg Neurol. 1993 Feb;39(2):133-7. doi: 10.1016/0090-3019(93)90091-e.

DOI:10.1016/0090-3019(93)90091-e
PMID:8351626
Abstract

A case of congenital subclavian steal syndrome associated with an anomalous right-sided aorta is reported. A 41-year-old man complaining of vertigo and a loss of consciousness was admitted. Physical examination revealed a blood pressure differential between the arms that was 20 mm Hg less in the left. Aortography showed a right aortic arch from which arose the right subclavian and both common carotid arteries. The left subclavian artery did not opacify. Right vertebral angiography showed retrograde filling of the left vertebral. A left carotid-subclavian bypass was performed. Postoperatively, the patient is symptom free with equalized blood pressure.

摘要

报告了一例与右位主动脉异常相关的先天性锁骨下动脉盗血综合征病例。一名41岁男性因眩晕和意识丧失入院。体格检查发现双臂血压存在差异,左侧比右侧低20毫米汞柱。主动脉造影显示为右位主动脉弓,从该弓发出右锁骨下动脉和双侧颈总动脉。左锁骨下动脉未显影。右椎动脉造影显示左椎动脉逆行充盈。进行了左颈动脉-锁骨下动脉搭桥术。术后,患者症状消失,血压恢复正常。

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1
Congenital subclavian steal syndrome with anomaly of the aortic arch.先天性锁骨下动脉盗血综合征合并主动脉弓异常
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[Congenital subclavian steal syndrome: a case of right aortic arch with atretic aberrant left subclavian artery].先天性锁骨下动脉盗血综合征:一例右位主动脉弓合并左锁骨下动脉发育不全伴闭锁病例
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Left aortic arch with congenital isolation of the right subclavian artery.左位主动脉弓伴右锁骨下动脉先天性孤立。
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Right aortic arch with contralateral congenital subclavian steal syndrome.右位主动脉弓伴对侧先天性锁骨下动脉盗血综合征。
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Right aortic arch, isolated left common carotid and left subclavian arteries, and subclavian steal syndrome: a variant of polysplenia syndrome.右位主动脉弓、孤立的左颈总动脉和左锁骨下动脉以及锁骨下动脉窃血综合征:多脾综合征的一种变异型
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引用本文的文献

1
Congenital isolation of the subclavian artery in adults.成人锁骨下动脉先天性孤立
Tex Heart Inst J. 1997;24(1):58-61; discussion 61-3.