Arvay A, Lengyel M, Richter T, Lukács L
Országos Kardiológiai Intézet, Budapest.
Orv Hetil. 1993 Aug 29;134(35):1907-11.
Cor triatriatum sinistrum is a rare congenital cardiac anomaly in which a membrane divides the left atrium. Severity of the disease depends on the size of the opening on the membrane. The anomaly presents with severe pulmonary hypertension and prognosis is unfavourable without surgery. From 1976 through 1992, 5 adult patients were treated surgically in our institution. Cor triatriatum can be corrected surgically with a low mortality and excellent late results if an early preoperative diagnosis has been made. Clinical findings and cardiac catheterization do not provide sufficient data for the correct diagnosis. From a review of our experience it is concluded that echocardiography is superior to angiography for diagnosing cor triatriatum.
左房三房心是一种罕见的先天性心脏畸形,即有一隔膜将左心房分隔开。该病的严重程度取决于隔膜上开口的大小。此畸形表现为严重的肺动脉高压,若不进行手术,预后不佳。1976年至1992年期间,我院对5例成年患者实施了手术治疗。如果能早期做出术前诊断,左房三房心可通过手术矫正,死亡率低且远期效果良好。临床检查结果和心导管检查不能为正确诊断提供足够的数据。根据我们的经验回顾得出结论,超声心动图在诊断左房三房心方面优于血管造影。