Roussel P
Département de Biochimie, Faculté de Médecine de Lille.
Bull Acad Natl Med. 1993 Mar;177(3):395-402; discussion 402-3.
Chronic lung colonization in CF is specific and due mainly to Pseudomonas aeruginosa. Since no phagocytic or immunological abnormalities seem to be responsible for this specificity, it is possible that post-translational alterations of respiratory mucins biosynthesis occur and modify the affinity of mucins for Pseudomonas aeruginosa.