Yeoh G, Russell P, Wills E J, Fleming S
Department of Anatomical Pathology, Royal Prince Alfred Hospital, Sydney.
Pathology. 1993 Apr;25(2):197-202. doi: 10.3109/00313029309084800.
A rarely encountered but distinctive type of aggressive malignant tumor of childhood and adolescence has been recently described as occurring predominantly or exclusively intrabdominally. It is characterized by a generally diffuse pattern of growth of small cells with hyperchromatic nuclei, scanty cytoplasm, patchy epithelial differentiation, immunohistochemical co-expression of keratin and desmin intermediate filaments and a focal but pronounced desmoplastic stromal component. It is regarded as yet another variant in the group of small round cell tumors (SRCT) of infancy and childhood. This case report of a mass in the greater omentum of a 15 yr-old girl adds to the 33 cases already described in the English literature.
一种罕见但独特的儿童和青少年侵袭性恶性肿瘤最近被描述为主要或仅发生于腹腔内。其特征为小细胞呈弥漫性生长模式，细胞核深染，细胞质稀少，有局灶性上皮分化，角蛋白和结蛋白中间丝免疫组化共表达，以及局灶但明显的促纤维组织增生性间质成分。它被视为婴幼儿和儿童小圆形细胞肿瘤（SRCT）组中的又一变体。本病例报告了一名15岁女孩大网膜肿块，补充了英文文献中已描述的33例病例。
