Chiou Y Y, Wu J M, Wang J K, Wu M H, Ke W L, Yang Y J
Department of Pediatrics, National Cheng-Kung University Hospital, Tainan, Taiwan, R.O.C.
Zhonghua Min Guo Xiao Er Ke Yi Xue Hui Za Zhi. 1993 May-Jun;34(3):204-10.
Two neonates with a combination of truncus arteriosus and interruption of the aortic arch, so-called type A4 of the Van Praagh classification, are reported. Both presented as tachypnea, poor appetite and increasing cyanosis during the first week of life. The combination of these defects significantly increases the surgical risk. Di-George syndrome was noted in one patient, who presented with hypocalcemia and T cell dysfunction. Autopsy confirmed this diagnosis.
报道了两名患有共同动脉干合并主动脉弓中断的新生儿，即范普拉格分类中的A4型。两名患儿在出生后第一周均表现为呼吸急促、食欲不佳和发绀加重。这些缺陷的组合显著增加了手术风险。其中一名患者被发现患有迪格奥尔格综合征，表现为低钙血症和T细胞功能障碍。尸检证实了这一诊断。
