Eguchi G, Shigemori M, Sugita Y, Kuramoto S, Uegaki M
Department of Neurosurgery, Kurume University School of Medicine, Japan.
No Shinkei Geka. 1993 Mar;21(3):247-50.
We reported a case of Turcot Syndrome (glioma polyposis) in a 19-year-old woman with nonfamilial polyposis coli and adenocarcinoma of the colon, and grade 3 astrocytoma in the right parietal lobe. The patient was admitted with the complaint of general convulsion after colostomy for polyposis and adenocarcinoma of the colon. CT scans on admission showed a large parietal tumor in the right side. Total removal was performed successfully and histological examination showed astrocytoma grade 3. One year after the operation, the tumor recurred. Conservative treatment failed to improve her condition and she died one year later. Turcot Syndrome (glioma polyposis) is very rare and only 10 cases have been reported in Japan. In this report, the clinical characteristics of this syndrome were discussed.
我们报告了一例Turcot综合征（胶质瘤息肉病），患者为一名19岁女性，患有非家族性结肠息肉病和结肠癌，右侧顶叶有3级星形细胞瘤。该患者因结肠息肉病和腺癌行结肠造口术后，因全身抽搐入院。入院时的CT扫描显示右侧顶叶有一个大肿瘤。成功进行了全切术，组织学检查显示为3级星形细胞瘤。术后一年，肿瘤复发。保守治疗未能改善她的病情，一年后她去世。Turcot综合征（胶质瘤息肉病）非常罕见，在日本仅报告过10例。在本报告中，对该综合征的临床特征进行了讨论。
