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在一例症状轻微的隐性先天性肌强直病例中,非诺特罗引发了肌强直。

Fenoterol precipitating myotonia in a minimally affected case of recessive myotonia congenita.

作者信息

Ricker K, Haass A, Glötzner F

出版信息

J Neurol. 1978 Dec 22;219(4):279-82. doi: 10.1007/BF00312981.

Abstract

Fenoterol is used in patients with premature labor to delay delivery. A young women treated with fenoterol developed severe generalized myotonia. Symptoms disappeared after medication had been stopped. In a later study myotonic discharges were found electromyographically in the muscles of the patient and her brother. Both suffered from subclinical recessive myotonia congenita (Becker). A heterozygous manifestation may be supposed.

摘要

羟苄羟麻黄碱用于早产患者以延迟分娩。一名接受羟苄羟麻黄碱治疗的年轻女性出现了严重的全身性肌强直。停药后症状消失。在后来的一项研究中,通过肌电图检查在该患者及其兄弟的肌肉中发现了肌强直放电。两人都患有亚临床隐性先天性肌强直(贝克尔型)。可以推测存在杂合子表现。

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