Kerkar P, Dalvi B, Kale P
Department of Cardiology, King Edward VII Memorial Hospital, Parel, Bombay, India.
Chest. 1993 Jan;103(1):279-80. doi: 10.1378/chest.103.1.279.
Interruption of the aortic arch is a rare and usually lethal cardiac malformation. We report a rare case of a patient with IAA distal to the left subclavian artery associated with double outlet right ventricle, subaortic VSD and patent DA who survived to adulthood. In this patient, the complete diagnosis was made by cardiac catheterization and angiocardiography. We discuss the probable mechanisms, diagnostic problems and therapeutic implications of such long survival.
主动脉弓中断是一种罕见且通常致命的心脏畸形。我们报告了一例罕见病例，患者主动脉弓中断发生在左锁骨下动脉远端，合并右心室双出口、主动脉瓣下室间隔缺损及动脉导管未闭，存活至成年。该患者通过心导管检查和心血管造影术得以明确诊断。我们讨论了如此长期存活的可能机制、诊断问题及治疗意义。
