Applebaum M M, Thaler M M
Am J Dis Child. 1977 Mar;131(3):295-6. doi: 10.1001/archpedi.1977.02120160049008.
We report Reye syndrome in an 11-year-old boy whose first symptoms were generalized convulsions and coma without clinical or laboratory evidence of liver disease. Serum glutamic oxaloacetic transaminase and lactate dehydrogenase (LDH) values increased strikingly on the third day after the onset of coma. These enzymatic changes were associated with prolongation of prothrombin time. A rise in blood ammonia concentrations began on the fourth day of coma. The diagnosis of Reye syndrome was confirmed by a liver biopsy and at autopsy. This case demonstrates that encephalopathy in Reye syndrome can develop prior to detectable hepatic involvement, and suggests that factors unrelated to generalized liver damage may occasionally play a role in the pathogenesis of this obscure disorder.
我们报告了一名11岁男孩的瑞氏综合征,其最初症状为全身性惊厥和昏迷,且无肝脏疾病的临床或实验室证据。昏迷发作后第三天,血清谷氨酸草酰乙酸转氨酶和乳酸脱氢酶(LDH)值显著升高。这些酶变化与凝血酶原时间延长有关。昏迷第四天血氨浓度开始升高。肝活检和尸检证实了瑞氏综合征的诊断。该病例表明,瑞氏综合征中的脑病可在可检测到的肝脏受累之前出现,并提示与广泛性肝损伤无关的因素偶尔可能在这种不明疾病的发病机制中起作用。