Gosseye S, De Meyer R, Maldague P
Helv Paediatr Acta. 1976 Apr;30(6):509-13.
A 2 1/2-year-old child died after an illness of three days duration, characterized by a sudden onset, vomiting, coma and a striking hyperammonemia. At autopsy, the liver was practically normal. This is a further example of Reye's syndrome with only minimal fatty infiltration of the liver. It appears that the classical massive and diffuse fatty degeneration of the liver is not an essential feature of the syndrome. The evidence for this is discussed.
一名2岁半儿童在患病三天后死亡,其病症特点为起病急、呕吐、昏迷及显著的高氨血症。尸检时,肝脏基本正常。这是瑞氏综合征的又一实例,肝脏仅有极少的脂肪浸润。看来,肝脏典型的大量弥漫性脂肪变性并非该综合征的必要特征。对此的证据将予以讨论。