Meister L, Duarte A M, Davis J, Perez J L, Schachner L A
Department of Pediatrics, University of Miami School of Medicine, FL 33101.
J Am Acad Dermatol. 1993 Jan;28(1):93-5. doi: 10.1016/0190-9622(93)70017-n.
All forms of cutaneous T-cell lymphoma are rare in children. We describe an 11-year-old girl who had generalized exfoliative erythroderma, intense pruritus, peripheral lymphadenopathy, mycosis cells in the skin and lymph nodes, and Sézary cells in the peripheral blood. Results of a biopsy specimen of involved skin showed changes consistent with mycosis fungoides. A classic case of Sézary syndrome has not previously been reported in childhood or preadolescence.