Pilcher R
Princess Alexandra Hospital, Wroughton, Swindon, Wilts.
J R Army Med Corps. 1993 Feb;139(1):20-4. doi: 10.1136/jramc-139-01-06.
A case of basal cell naevus syndrome is presented. The jaw cysts were proved histopathologically to be odontogenic keratocysts. The multiple naevoid lesions on the skin were identified as basal cell carcinoma. Intracranial calcification is illustrated to a degree not previously reported in a case with this syndrome. The importance of identifying this syndrome is discussed and its presentation in the Falkland Islands is reported.
本文报告了1例基底细胞痣综合征病例。经组织病理学证实，颌骨囊肿为牙源性角化囊肿。皮肤上的多发性痣样病变被确诊为基底细胞癌。文中展示了该综合征患者颅内钙化程度，此前未见类似病例有如此程度的报道。本文讨论了识别该综合征的重要性，并报告了其在福克兰群岛的临床表现。
